Child pemphigus vulgaris. Case presentation

Authors

Keywords:

youth pemphigus vulgaris, immune disorder, skin diseases

Abstract

It was presented a clinical case of a 16-year-old female patient with a pemphigus vulgaris diagnosis at the General Teaching Hospital “Dr. Agostinho Neto”, Guantanamo, July-October 2017. Child-youth pemphigus vulgaris is not very frequent in our country (0.1-0.5%); however, it is the most common and serious form of pemphigus. It occurs most frequently in the fourth and sixth decade of life, being rare in children. It has no sex or race predilection, it is associated with immune disorders. It is characterized by the appearance of relatively tight blisters, on skin and mucosa membranes, which later break and form erosions of macerated surfaces, covered with whitish material and very painful, making patients weak, and along with the loss of electrolytes through skin lesions, can lead to death.

Downloads

Download data is not yet available.

References

Valencia-Ocampo O, Velásquez-Lopera M. Inmunopatogenia del pénfigo vulgar y el pénfigo foliáceo. Iatreia [en línea]. 2011 [citado 1 Ene 2020]; 4(3):272-286. Disponible en: http://www.scielo.org.co/scielo.php?script=sci_abstract&pid=S0121-07932011000300006&lng=e&nrm=iso&tlng=e

Herrera-López I, Miranda-Tarrago J. Pénfigo vulgar, criterios actuales. Rev Hab Ciencias Méd [en línea]. 2009 [citado 1 Ene 2020]; 8(5):45-51. Disponible en: http://scielo.sld.cu/pdf/rhcm/v8s5/rhcm08509.pdf

Sánchez-Pérez J, García-Diez A. Pénfigo. Actas Dermo-Sifiliogr [en línea]. 2005 Jul [citado 1 Ene 2020]; 96(6):329-356. Disponible en: https://www.actasdermo.org/es-penfigo-articulo-resumen-13078495

Stanley J, Amagai M. Pemphigus, bullous impétigo and the Staphylococcal scalded-skin syndrome. N Engl J Med [en línea]. 2006 [citado 1 Ene 2020]; 355:1800-1810. DOI: 10.1056/NEJMra061111

Hertl M, Sitaru C. Pathogenesis, clinical manifestations, and diagnosis of pemphigus. Up to Date [en línea]. 2018. [citado 1 Ene 2020; actualizado 5 Mar 2020]. Disponible en: https://www.uptodate.com/contents/pathogenesis-clinical-manifestations-and-diagnosis-of-pemphigus

Hertl M, Geller S. Initial management of pemphigus vulgaris and pemphigus foliaceus. Up to Date [en línea]. 2017. [citado 1 Ene 2020; actualizado 5 Mar 2020]. Disponible en: https://www.uptodate.com/contents/initial-management-of-pemphigus-vulgaris-and-pemphigus-foliaceus?search=initial%20management-of-pemphigus-vulgaris-and-pemphigus%20folia&source=search_result&selectedTitle=2~150&usage_type=default&display_rank=2

Tamgadge S, Tamgadge A, Bhatt D, Bhalerao S, Pereira T. Pemphigus vulgaris. Cont Clin Dent [en línea]. 2011 [citado 1 Ene 2020]; 2(2):134-137. Disponible en: http://www.contempclindent.org/text.asp?2011/2/2/134/83074

Aldama A, Aquino N. Pénfigo. Tend Med [en línea]. 2016 [citado 1 Ene 2020]; 11(11):102-106. Disponible en: http://tendenciasenmedicina.com/Imagenes/imagenes11p/art_17.pdf

Sirois D, Leigh J, Sollecito T. Oral pemphigus vulgaris preceding cutaneous lesions: recognition and diagnosis. J Am Dent Assoc [en línea]. 2000 [citado 1 Ene 2020]; 131:1156-1160. DOI: 10.14219/jada.archive.2000.0349

Castellanos-Iñiguez A. Guevara-Gutiérrez E. Pénfigo vulgar. Dermatol Rev Mex [en línea]. 2011 [citado 1 Ene 2020]; 55(2):73-83. Disponible en: https://www.medigraphic.com/pdfs/derrevmex/rmd-2011/rmd112d.pdf

Huang A, Madan R, Levitt J. Future therapies for pemphigus vulgaris: Rituximab and beyond. J Am Acad Dermatol [en línea]. 2016 [citado 1 Ene 2020]; 74(4):746-753. DOI: 10.1016/j.jaad.2015.11.008

Peña-Ortiz J, Romero-Álvarez J, Trujillo-Padilla S. Abordaje terapéutico dermatológico ambulatorio del pénfigo vulgar en adultos. En: Guía de práctica clínica. México: Instituto Mexicano Seguro Social; 2013. p.1-8. [citado 1 Ene 2020]. Disponible en: https://docplayer.es/79806858-Abordaje-terapeutico-dermatologico-ambulatorio-del-penfigo-vulgar-en-adultos.html

Atzmony L, Hodak E, Leshem Y, et al. The role of adjuvant therapy in pemphigus: A systemic review and meta-analysis. J Am Acad Dermatol [en línea]. 2015 [citado 1 Ene 2020]; 73(2):264-271. DOI: 10.1016/j.jaad.2015.04.038

Gregoriou S, Efthymiou O, Stefanaki C, Rigopoulos D. Management of pemphigus vulgaris: challenges and solutions. Clin Cosmetic Inv Dermatol [en línea]. 2015 [citado 1 Ene 2020]; 8:521-527. DOI: 10.2147/CCID.S75908

Doukaki S, Platamone A, Alaimo R, Bongiorno M. Mycophenolatemofetil and enteric coated mycophenolate sodium in the treatment of pemphigus vulgaris and pemphigus foliaceus. J Dermatol Treat [en línea]. 2015 [citado 1 Ene 2020]; 26(1):67-72. DOI: 10.3109/09546634.2014.880395

Kayani M, Aslam A. Bullous pemphigoid and pemphigus vulgaris. BMJ [en línea]. 2017 [citado 1 Ene 2020]; 357:j2169. DOI: 10.1136/bmj.j2169

Hertl M, Eming R. Management of refractory pemphigus vulgaris and pemphigus foliaceus. Up to Date [en línea]. 2017 [citado 1 Ene 2020]. Disponible en: https://www.uptodate.com/contents/management-of-refractory-pemphigus-vulgaris-and-pemphigus-foliaceus

McCarty M, Fivenson D. Two decades of using the combination of tetracycline derivatives and niacinamide as steroid-sparing agents in the management of pemphigus: defining a niche for these low toxicity agents. J Am Acad Dermatol [en línea]. 2014 [citado 1 Ene 2020]; 71(3):475-479. DOI: 10.1016/j.jaad.2014.04.040

Korman N. Pemphigus. J Am Acad Dermatol [en línea]. 1988 [citado 1 Ene 2020]; 18(6):1219-1238. DOI: 10.1016/s0190-9622(88)70128-0

Matos-Cruz R, Bascones-Martinez A. Pénfigo: Una revisión de la literatura. Av Odontoestomatol [en línea]. 2009 [citado 1 Ene 2020]; 25(2):67-82. Disponible en: http://scielo.isciii.es/pdf/odonto/v25n2/original2.pdf

Published

2020-05-10

How to Cite

1.
Mercadilla-Ramírez S. Child pemphigus vulgaris. Case presentation. Gac méd estud [Internet]. 2020 May 10 [cited 2024 Jul. 3];1(1). Available from: https://revgacetaestudiantil.sld.cu/index.php/gme/article/view/21

Issue

Section

Case reports